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| Regel 18: |
Regel 18: |
| * Late potentialen op een [signal averaged ECG] | | * Late potentialen op een [signal averaged ECG] |
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| dit moet nog verbeterd worden
| | De European Society of Cardiology heeft een lijst van diagnostische criteria opgesteld waar iemand aan moet voldoen om de diagnose ARVD te stellen. Belangrijke kenmerken hierbij zijn: |
| | | * Indien ARVD bij een familielid is vastgesteld bi obductie |
| {| width="623" border="1" cellspacing="1" cellpadding="1"
| | * Plotse hartdood (<35 jaar) bij een familielid |
| | width="34%" valign="center" |
| | * Sustained of non-sustained VT's met een linker bundeltakblok |
| | width="37%" valign="center" | '''<font size="2"> Major </font>'''
| | * Frequente extrasystolen (>1000 / 24 uur op een [Holter] monitor) |
| | width="29%" valign="center" | '''<font size="2"> Minor </font>'''
| | * Verwijding en verminderde pompkracht van de rechter hartkamer |
| |-
| | * Kleine aneurysmata (ballonvormige verwijdingen) van de rechter hartkamerwand |
| | width="34%" valign="center" |
| |
| Global / regional dysfunction and structural alterations (imaging techniques)
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| | width="37%" valign="center" |
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| Severe right ventricular dilatation Decrease in RV EF with normal/nearly normal LV EF<br />RV localised aneurysms (akinetic / diskinetic areas with systolic bulging)<br />Severe RV segmental dilatation
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| | width="29%" valign="center" |
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| Mild global RV dilatation and/or decrease in RV EF with normal LV<br />Mild RV segmental dilatation<br />Regional RV hypokinesia
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| |-
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| | width="34%" valign="center" |
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| Tissue characterization of the RV myocardium
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| | width="37%" valign="center" | Fatty infiltration of the RV myocardium
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| | width="29%" valign="center" |
| |
| |-
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| | width="34%" valign="center" |
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| Repolarization abnormalities
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| | width="37%" valign="center" |
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| | width="29%" valign="center" | Inverted T waves in V2-V3 (if age > 12 yrs, in the absence of right bundle branch block)
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| |-
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| | width="34%" valign="center" |
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| Depolarization/conduction abnormalities
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| | width="37%" valign="center" | Epsilon waves, widening of the QRS complex (>110ms) in V1-V3
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| | width="29%" valign="center" | Late potentials
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| |-
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| | width="34%" valign="center" |
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| Arrhythmias
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| | width="37%" valign="center" |
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| | |
| | width="29%" valign="center" |
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| Sustained/non-sustained ventricular tachycardia with left bundle branch block morphology <br /><br />Frequent ventricular ectopics (>1000/24hours)
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| |-
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| | width="34%" valign="center" | Family history
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| | width="37%" valign="center" | Family history with anatomic confirmation (autopsy, surgery)
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| | width="29%" valign="center" | Sudden death in <35 years, with suspicion of ARVC<br />Family history of ARVC (clinical diagnosis)
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| |}
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| ===Behandeling=== | | ===Behandeling=== |